### CincyKidsRad

Cincinnati Children's Radiology

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## Pancreatoblastoma

### Image description

Axial contrast-enhanced CT of the abdomen shows a large mass arising from the tail of the pancreas (arrow). Metastatic lesions are present in the liver (arrowhead). Metastatic lymphadenopathy encases the vasculature of the left kidney.

### Teaching point

Pancreatoblastoma is a rare malignant pancreatic tumor of infancy and early childhood. It is associated with Beckwith-Wiedemann syndrome and familial adenomatous polyposis. Serum alpha-fetoprotein is frequently elevated and can be useful for diagnosis and treatment monitoring. At presentation, the tumor is often large and metastatic, commonly involving the liver and regional lymph nodes.

### Diagnosis added by author

**Show diagnosis**  
Pancreatoblastoma

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### More about this case

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