Pancreatoblastoma | Figure 1
CincyKidsRad
Cincinnati Children's Radiology
Pancreatoblastoma
Image description
Axial contrast-enhanced CT of the abdomen shows a large mass arising from the tail of the pancreas (arrow). Metastatic lesions are present in the liver (arrowhead). Metastatic lymphadenopathy encases the vasculature of the left kidney.
Teaching point
Pancreatoblastoma is a rare malignant pancreatic tumor of infancy and early childhood. It is associated with Beckwith-Wiedemann syndrome and familial adenomatous polyposis. Serum alpha-fetoprotein is frequently elevated and can be useful for diagnosis and treatment monitoring. At presentation, the tumor is often large and metastatic, commonly involving the liver and regional lymph nodes.
Diagnosis added by author
Show diagnosis
Pancreatoblastoma
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