AP (image 1) and cross-table lateral (image 2) show an abnor | Figure 1

CincyKidsRad

Cincinnati Children's Radiology

AP (image 1) and cross-table lateral (image 2) show an abnormal abdominal wall with bulging of the flanks on the AP view and a concave appearance of the abdomen with wrinkled redundant skin along the anterior abdominal wall. The radiographic findings are consistent with prune belly syndrome. Prune belly syndrome is a disorder caused by a lack of muscles in the anterior abdominal wall. Other findings include undescended testes, urinary tract abnormalities, and pulmonary hypoplasia. #FridayQuizDay #Quiz #FridayQuiz

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Abdominal radiograph (image 1) in a patient with Eagle-Barrett syndrome shows an abnormal configuration of the abdominal wall with lateral bulging of the flanks, and bowel spread across the abdomen extending to both the right and left. AP (image 2) and oblique (image 3) images from a voiding cystourethrogram reveal an abnormal configuration of the urinary bladder with grade 5 vesicoureteral reflux into both ureters. Eagle-Barrett syndrome, characterized by a triad of deficient abdominal musculature, cryptorchidism, and urinary tract anomalies, presents with an abnormal abdominal configuration due to the deficient abdominal wall musculature. Urinary tract anomalies can include pelvocaliectasis, ureterectasis, vesicoureteral reflux, and renal dysplasia. Respiratory complications are also common.

This male infant was found to have prune belly syndrome (PBS) at birth, a rare disorder characterized by the complete or partial absence of abdominal muscles, undescended testes, and a dilated urinary tract. Also called Eagle-Barrett syndrome, it results in a large, lax abdomen with a thin abdominal wall through which intestinal loops may be seen. PBS affects up to 1 in 30,000 live births, with over 95% of cases occurring in male infants. There is a broad spectrum of severity ranging from undescended testes and minimal laxity of the abdominal wall to stillbirth.

#Abdominal adhesions in chronic, intermittent appendicitis patient. Had pulled up #Bowel to anterior abdominal wall

Patient comes to the ED complaining of palpitations. Refers to have a "loose kidney". At palpation, it seems that he has agenesy of abdominal muscles. Would that be a milder form of Prune-belly syndrome? Refers to have passed for one surgery when a child, doesn't know which.