Radiograph of the pelvis and skull shows multiple foci of fi | Figure 1

CincyKidsRad

Cincinnati Children's Radiology

Radiograph Findings

Radiograph of the pelvis and skull shows multiple foci of fibrous dysplasia (arrows and arrowhead). The lesion in the occiput (arrowhead) is causing thickening of the outer table of the skull.

Polyostotic fibrous dysplasia is associated with McCune-Albright syndrome. This syndrome is associated with a clinical triad of café-au-lait spots, polyostotic fibrous dysplasia, and precocious puberty. Other potential endocrine disorders include hyperthyroidism, acromegaly, and Cushing syndrome.

Similar Cases

1. Tac 3D
   Details: Female patient, 23 yo, comes to consult with bone mass growth since she was 8yo. Large height for her age. Postox of tracheotomy and osteotomy + bone regularization 3 years ago with the diagnosis of Fibrous Dysplasia in another center. Could it be secondary to a syndrome and which one?

2. 9 yo boy with fibrous dysplasia.
   Details: History of head shape abnormality. CT shows findings of groundglass opacity and bony expansion. Plan to delay surgery unless neurological symptoms develop.

3. Young man with a mass-like enlargement of the 7th rib.
   Details: Rare disorder called Fibrous Dysplasia. No cure but monitoring for additional growth.

4. Radiograph of the hand.
   Details: Expansile lucent lesion of the index finger, differential diagnosis includes polyostotic fibrous dysplasia or multiple enchondromas.

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