Frontal chest radiograph in a patient with neurofibromatosis | Figure 1

CincyKidsRad

Cincinnati Children's Radiology

Frontal chest radiograph in a patient with neurofibromatosis type I (NF1) shows a short angular upper thoracic dextroscoliosis. An adjacent soft tissue mass (white) and multiple dysplastic ribs are noted. Coronal T2-weighted MR image in the same patient with NF1 shows a predominantly hyperintense mass (white) infiltrating the soft tissues adjacent to the spinal curvature and the left chest wall. A “target” appearance (yellow) is seen within one component of the mass, typical of plexiform neurofibromas viewed in cross-section. #NeuroWednesday

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