CincyKidsRad

Cincinnati Children's Radiology

Eagle Barrett syndrome

Abdominal radiograph (image 1) in a patient with Eagle-Barrett syndrome shows an abnormal configuration of the abdominal wall with lateral bulging of the flanks, and bowel spread across the abdomen extending to both the right and left. AP (image 2) and oblique (image 3) images from a voiding cystourethrogram reveal an abnormal configuration of the urinary bladder with grade 5 vesicoureteral reflux into both ureters. Eagle-Barrett syndrome, characterized by a triad of deficient abdominal musculature, cryptorchidism, and urinary tract anomalies, presents with an abnormal abdominal configuration due to the deficient abdominal wall musculature. Urinary tract anomalies can include pelvocaliectasis, ureterectasis, vesicoureteral reflux, and renal dysplasia. Respiratory complications are also common.

Similar cases

Coronal (image 1) and axial (image 2) images from fetal MRI show an abnormal appearance of the kidneys (arrows) with multiple cortical cysts and massive enlargement of the ureters (arrowheads). On postnatal voiding cystourethrogram (image 3) bladder rupture is visible. Contrast fills the urinary bladder (arrowhead). There is leakage of contrast (arrow) from the right lateral aspect of the bladder and pooling (dashed arrow) within the right lower quadrant. Posterior urethral valves is the most common cause of fetal bladder outlet obstruction. Bladder rupture is an uncommon manifestation of this obstruction. High-grade vesicoureteral reflux is more common and leads to kidney damage. Posterior urethral valves as the most common cause of chronic kidney injury in children.

Chest radiograph in a child with Tetralogy of Fallot displays the characteristic 'boot-shaped' configuration of the heart with an upturned cardiac apex. Tetralogy of Fallot is a combination of four anomalies: ventricular septal defect, right ventricular outflow tract obstruction, an overriding aorta, and right ventricular hypertrophy. This heart shape results from the right ventricular hypertrophy and a small pulmonary artery.

purple urine bag syndrome, as you can see it has a alarming purple colored urine. It occurs in people with prolonged Urinary Catheterization and recurrent Urinary Tract Infection.

Voiding image from a voiding cystourethrogram in a girl with a history of multiple urinary tract infections and daytime wetting shows a spinning top configuration of the urethra (arrow). A "spinning top" urethra occurs due to functional discoordination of the external sphincter. This configuration can be suggested with dilation of the posterior urethra and relative narrowing at the external urethral sphincter.