2024 Friday Quiz 5 Answer | Figure 1

CincyKidsRad

Cincinnati Children's Radiology

2024 Friday Quiz 5 Answer

Sagittal (image 1), coronal (image 2), and axial (image 3) T2 weighted images as well as axial post contrast (image 4) and diffusion weighted image (image 5) show the tectal mass. Overall, the mass is mostly solid with small T2 hyperintense foci, mild heterogeneous enhancement, and restricted diffusion. Atypical teratoid/rhabdoid tumors (ATRT) typically present in young children. The lesions may mimic medulloblastoma but can occur in other locations within the brain. On imaging, they are often enlarged and heterogeneous. The tumor is typically caused by inactivation of the INI/SMARCB1 gene. ATRT tumors are associated with rhabdoid tumors of the kidney or liver. Thus, abdominal ultrasound is often performed after ATRT diagnosis. Other tumor types associated with INI/SMARCB1 inactivation include epithelioid sarcomas, chordomas, and renal medullary carcinoma.

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